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· DOS Abstracts
Operative management of femoral Focal Fibrocartilagi-
nous Dysplasia in children
Line Kjeldgaard Pedersen, Jens Svendsson, Mindaugas Mizukis, Søren Harving
Børne ortopædkirurgisk afdeling, Aalborg Universitetshospital; Børne ortopæd-
kirurgisk afdeling, Aalborg Universitetshospital; Børne ortopædkirurgisk afdel-
ing, Aalborg Universitetshospital; Børne ortopædkirurgisk afdeling, Aalborg Uni-
versitetshospital
Background:
Focal Fibrocartilaginous Dysplasia (FFCD) is an extremely rare
disorder causing angular deformities of the long bones in children. The condition
is defined by a diafyseal fibrous tether preventing the natural sliding of perios-
teum during growth resulting in a hemiepiphysiodesis effect causing angular
deformities. The location of the lesions are predominantly in the proximal tibia,
although distal femoral, humeral and ulnar cases have been reported. No defini-
tive consensus has been proposed regarding treatment. Spontaneus resolution
of the deformity is primarily reported for tibial cases. Operative management
may include excision of the tether, periosteum and curettage as well as correc-
tive osteotomies.
Purpose / Aim of Study:
To report on a case of femoral FFCD with operative
management.
Materials and Methods:
Operative management of a confirmed case of FFCD
is presented with preoperative radiographical and Magnetic Resonance Image
(MRI) evaluation in addition to a thorough peroperatively illustration of the
operative management. Furthermore the postoperative angular correction is
documented.
Findings / Results:
A 22 months old boy referred for specialist children’s or-
thopaedic evaluation presented with progressive unilateral genu vara. Clinical
evaluation showed bowing of the distal femur and subsequent radiographical
examination revealed a lesion on the distal medial femoral diaphysis with an an-
gular medial deformity. An MRI was performed under general anesthesia reveal-
ing a fibrous tether confirming the diagnosis of FFCD. The tether was treated
surgically by excision of both the tether and surrounding periosteum and curet-
tage.
Conclusions:
FFCD with a medial femoral location can be operatively managed
by open excision of the tether and medial periosteal release with subsequent
correction of the angular deformity.
No conflicts of interest reported
58.